The importance of adequate dental management to the patient with Cleidocranial Dysostosis: Case report
International Journal of Development Research
The importance of adequate dental management to the patient with Cleidocranial Dysostosis: Case report
Received 18th March, 2018; Received in revised form 07th April, 2018; Accepted 20th May, 2018; Published online 30th June, 2018.
Copyright © 2018, Alexandre Cândido da Silva et al. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
Cleidocranial Dysostosis (CCD) is characterized as a rare autosomal dominant genetic syndrome with no gender preference, characterized by a defect in the gene CBFA1 of chromosome 6p21, which modulate the formation of osteoblasts. Its clinical characteristics are clavicle aplasia or hypoplasia, changes in skeletal level with influence on the anatomical structure of the wearer and polydontia. There is no specific treatment, and the main conduct is to offer the best possible quality of life to the bearer, and this involves oral health. In this context, dentistry has an important role, mainly in what concerns the maintenance of the developed dental organs besides the physiological quantity (polydontia) due to the dysfunction. Thus, the present article aims to present the main characteristics of the DCC and report a case in which dental care was important for the improvement of the quality of life of the bearer.
